AMBIGUITE SEXUELLE DE DECOUVERTE TARDIVE A L’HOPITAL SOMINE DOLO DE MOPTI (MALI) A PROPOS D’UN CAS.

Dramane CISSE, Abdoulaye TRAORE, Honoré BERTHE, Mamadou COULIBALY, Amadou KASSOGUE, Moussa Salif DIALLO, Mamadou Lamine DIAKITE, Bréhima TRAORE, Djibril TRAORE, Karifala HAÏDARA, Aly TEMBELY, Zanafon OUATTARA

Résumé


RESUME

Les anomalies de la différenciation sexuelle ou Disorders of Sex Development (DSD) anciennement connues sous le nom d’ambiguïté sexuelle sont des conditions rares dans notre pratique. Nous rapportons un cas de 46 XY DSD,  pseudo-hermaphrodisme mâle, élevé comme fille, marié et venu consulter pour infertilité primaire. A la lumière de ce cas pris en charge dans ses aspects chirurgicaux et psychologiques et à travers une revue de la littérature, nous posons le problème de l’information de la patiente et de sa famille sur son sexe génomique dans un contexte de famille traditionnelle africaine.


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